Abstract Objective: To study the relationship of abdominal great vessels abnormalities, pediatric heterotaxy and congenital cardiovascular diseases(CCVD) by observing the positional relationship of inferior vena cava(IVC), abdominal aorta(AO) and vena azygos from subxiphoid view． Methods: Ninety-one cases of pediatric abdominal great vessels abnormalities diagnosed by ultrasonic examination and confirmed by MSCT, operation or autopsy were analyzed． These cases were divided into the following three categories. Type Ⅰ: absence of IVC and dilatation of azygos vein. Type Ⅱ: AO and IVC are on the same side of spine. Type Ⅲ: situs inversus of AO and IVC． The relationship of great vessels, heterotaxy and CCVD from different subxiphoid views were analyzed． Results: In the 91 cases of pediatric abdominal great vessels abnormalities observed from subxiphoid view, there were 8 cases of type Ⅰ， including 7 cases of CCVD with polysplenia and left isomerism, 1 case of normal spleen and heart; 29 cases of type Ⅱ, including 27 cases of asplenia syndrome, 29 cases of CCVD with right isomerism． Fifty-four cases of type Ⅲ, including 53 cases of situs inversus viscerum, 27 cases of CCVD with 1 case of asplenia syndrome and left isomerism. Conclusions: Abnormalities of abdominal great vessels often imply heterotaxy or situs inversus with different types of CCVD． It should be a routine inspection section for pediatric CCVD．
WU Ming-jun,GUO Dan-yang,LIU Chang, et al. Research on relationship of abdominal great vessels abnormalities, pediatric heterotaxy syndrome and#br# congenital cardiovascular diseases[J]. JOURNAL OF CHINA MEDICAL IMAGING, 2016, 27(7): 475-477.
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