Abstract Objective: To investigate the imaging features of alveolar soft part sarcoma(ASPS) in skull. Materials and Methods: The CT and MRI of eight patients with ASPS in skull confirmed by pathology were analyzed retrospectively. Results: All patients were shown excentric growth with pushing the scalp soft tissue and unclear margins abutting upon duramater. On CT scanning, six primary ASPSs were shown soft tissue mass with heterogeneous density, in which contained residual bone and uncompleted bony shell(n=6). The bone destruction was mainly osteolytic destruction(n=6). Two secondary ASPSs were shown soft tissue mass with homogeneous density and osteolytic destruction(n=2). On MRI scanning, six primary ASPSs were shown mushroom sign(n=6). The tumors appeared as hyper-intensity on T2WI, iso-intensity on T1WI and hyper-intensity on DWI(n=6). There were patchy hyper intensity areas, punctual/stripy hypo-intensity areas(n=4), clustered vessel signals(n=2) in tumors on T2WI. Inhomogeneous enhancement was seen on contrast-enhanced scan in six cases. Dural tail sign was seen in both side of the tumor(n=6). Two secondary ASPSs were shown orbicular-ovate mass(n=2). The tumors appeared as iso-intensity on T2WI and iso-intensity on T1WI(n=2). Homogeneous enhancement was seen on contrast-enhanced scan in two cases. The mean ADC value of six primary ASPSs was 2.19×10-4 mm2/s. The mean ADC value of two secondary ASPSs was 1.76×10-4 mm2/s. MRV was shown superior sagittal sinus pushed with a large number of drainage veins in the tumors. Conclusion: ASPS in skull was shown some typical imaging features. Combination the imaging features, clinical findings and pathology are helpful to the diagnosis the disease.
LI Yang,HAO Da-peng,SHI Xiang-long, et al. The imaging manifestations of alveolar soft part sarcoma in skull[J]. JOURNAL OF CHINA MEDICAL IMAGING, 2016, 27(8): 584-588.
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