Abstract：Objective: To evaluate the diagnostic value of the imaging examination of aorto-pulmonary septal defect and aortic origin of the right pulmonary artery with interruption of the aortic arch. Methods: Reviewed clinical data from medical records for 7 patients who had been treated in Wuhan Asia Heart Hospital between 2005 and 2013. Results: By UCG and CT, all cases were diagnosed as type A interruption of the aortic arch(according to celoria and patton’s classification), type Ⅱ aorto-pulmonary septal defect(according to Ho classification) and aortic origin of the right pulmonary artery. By cardiac catheterization, 3 of 4 patients were considered as severe pulmonary hypertention and gave up the operation, other 4 patients were treated as radical surgery. Conclusions: The combination of UCG and CT is a reliabe technique in the diagnosis of aorto-pulmonary septal defect and aortic origin of the right pulmonary artery with interruption of the aortic arch. The decision for surgery should be based on the combined information from cardiac catheterization and cardiovascular angiography. Pulmonary artery pressure and resistance are the most important factors that have great effects on the duration of surgery and the outcome.
余正春，马小静，夏 娟，李 菁. 主-肺动脉间隔缺损及右肺动脉起源于升主动脉合并主动脉弓离断的影像学诊断[J]. 中国临床医学影像杂志, 2016, 27(4): 260-262.
YU Zheng-chun, MA Xiao-jing, XIA Juan, LI Jing. The imaging examination of aorto-pulmonary septal defect and aortic origin of the right pulmonary artery with interruption of the aortic arch. JOURNAL OF CHINA MEDICAL IMAGING, 2016, 27(4): 260-262.
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