Prenatal ultrasonographic diagnosis of fetal right isomerism syndrome
LI Xue-lei, MU Zhong-ping, HUANG Ting
Maternal and Child Health Care Hospital Affiliated to Medical University of Anhui, Department of Ultrasound,
Anhui Province Maternal and Child Health Hospital, Hefei 230001, China
Abstract Objective: To investigate the prenatal ultrasonographic features of the right isomerism syndrome and to improve its prenatal detection rate. Methods: Ultrasonographic features of 11 cases of fetal isomerism in our hospital from April 2015 to May 2017 was analyzed. Results: In 11 cases of right isomerism syndrome, there were 10 cases of malposition of chest and abdominal organs(10/11). In 6 cases, the space between the gastric bubble and the spinal column was narrow, showing an adjacent relationship(6/11). Eleven cases were complicated with heart malformations and venous anomalies. Eight cases had pulmonary venous abnormalities, including 4 cases of the formation of the common pulmonary vein draining into the right atrium. Three cases had extracardiac malformations, including cleft lip, hiatal hernia and intestinal duplication. All 11 cases were confirmed by induction of labor or intrauterine MRI. Conclusions: Fetus with right isomerism syndrome has its characteristic cardiac malformation, and abnormal return of the body and pulmonary veins can help to evaluate its prognosis.
LI Xue-lei,MU Zhong-ping,HUANG Ting. Prenatal ultrasonographic diagnosis of fetal right isomerism syndrome[J]. JOURNAL OF CHINA MEDICAL IMAGING, 2018, 29(7): 498-500.
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