伴多器官受累的结节性硬化症影像学诊断

doi:10.12117/jccmi.2019.10.013

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Abstract Objective: To investigate the imaging features of tuberous sclerosis complex(TSC) with multiple organ involvement which may help improve the diagnostic efficacy. Methods: Clinical data and imaging findings of 10 patients with TSC confirmed by clinic were restrospectively analyzed. Results: Pulmonary lymphangioleiomyomatosis was found in 9 cases which were characterized by diffuse thin-wall cysts of different sizes in both lungs. Nine cases had multiple sclerosis in bones which was characterized by multiple nodular or patchy high density shadows. Renal angiomyolipomas were found in 6 cases, among which hepatic angiomyolipomas were found in 3 cases and bilateral multiple renal cysts were found in 1 case. Five cases were accompanied with typical subependymal nodules, 4 cases with abnormal signal intensity in white matter, and 4 cases with cortical and subcortical tubers. Conclusion: TSC with multiple organ involvement demonstrates certain imaging features, which may help the diagnosis of TSC.

Key words： Tuberous sclerosis Tomography, spiral computed Magnetic resonance imaging

Received: 06 November 2018

PACS:	Ｒ744.51
	Ｒ814.42
	Ｒ445.2

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	Articles by authors
	HU Jian-feng
	WANG Yu-ze
	LI Xin-chun
	BAO Ying-ying
	LEI Qiang
	WAN Qi
	ZOU Qiao

Cite this article:

HU Jian-feng,WANG Yu-ze,LI Xin-chun, et al. Imaging features of tuberous sclerosis with multiple organ involvement[J]. JOURNAL OF CHINA MEDICAL IMAGING, 2019, 30(10): 738-741.

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http://www.jccmi.com.cn/EN/10.12117/jccmi.2019.10.013 OR http://www.jccmi.com.cn/EN/Y2019/V30/I10/738

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