Abstract:Objective: To evaluate the diagnostic value for congenital pulmonary vein stenosis(PVS) by Doppler echocardiography. Methods: The echocardiography of 15 patients with PVS confirmed by catheterization, MRI or surgical operation were reviewed retrospectivey. Results: Among 15 PVS patients, six had right pulmonary vein stenosis, in whom 4 patients(66.7%) were diagnosed correctly by echocardiography, 2 patients(33.3%) were missed. Four patients had left pulmonary vein stenosis, all patients were diagnosed correctly. Five patients had bilateral pulmonary vein stenosis, four patients(80%) were diagnosed correctly and one patient with left pulmonary vein stenosis was missed. Four patients(26.7%) were simplex PVS, eleven patients(73.3%) were found to accompany with other cardiovascular anomalies. The most common associated anomalies were atrial septal defect, ventricular septal defect, patent ductus arteriosus, complete atrioventricular septal defect, double outlet of right ventricle. Conclusion: The reflux of pulmonary vein could be demonstrated and PVS could be diagnosed accurately by Doppler echocardiography.