1. Department of Radiology, Shengjing Hospital of China Medical University, Shenyang 110004, China;2. Department of Radiology, Linghai Hospital, Linghai Liaoning 121200, China
Abstract:Objective: To investigate CT imaging features of lymphangioleiomyomatosis. Materials and Methods: CT imaging data of 6 patients diagnosed as lymphangioleiomyomatosis were studied retrospectively including imaging of both chest and abdomen. Results: Multiple thin-walled cysts of different size were seen throughout the lung fields in an even distribution with normal intervening lung parenchyma in all the patients. Pneumothorax coexisted in 3 cases. In 1 case, pleural effusion was detected which was proved as chylothorax. Lymphadenopathy could be seen in 1 case. Three cases of kidney angioleiomyolipoma was found in abdominal CT imaging, among which lesions were multiple and bilateral in 2 cases. In these 3 cases, liver angioleiomyolipoma was found in one case and retroperitoneal angioleiomyolipoma was found in another case. Lymphangioleiomyoma of uterine broad ligament and retroperitoneum was found in 1 case. CT showed retroperitoneal lymphadenopathy in 1 case. Conclusion: lymphangioleiomyomatosis is a disease with characteristic imaging features, which is of great help for its diagnosis.