Abstract：Objective: By analyzing prenatal imaging characteristics, regular intrauterine monitoring, and following up of fetuses with congenital choledochal cysts, to explore the diagnostic value, differential diagnosis and clinical significance of prenatal ultrasound, thus providing the basis for prenatal consultation and neonatal treatment. Methods: 45 cases of fetuses with choledochal cysts were recruited in this study. Their prenatal ultrasonography were analyzed and compared with the postpartum follow-up results, pathological results, thus the prognosis and outcome were summarized. Results: 2 of the 45 cases were lost to followed up. 43 cases were recruited in this study. 35 of 43 cases were diagnosed with congenital choledochal cysts by neonatal abdominal ultrasound examination, with 34 cases confirmed by surgical pathology of congenital choledochal cysts and 1 case dying of kernicterus due to delay of surgical intervention. The prenatal ultrasound diagnosis coincidence rate was 81.4%(35/43). Seven cases were misdiagnosed, with a misdiagnosis rate of 16.3%(7/43), including 4 cases of hepatic cysts, 2 cases of congenital biliary atresia and 1 case of ovarian cyst, all of which were treated with surgery. One case(1/3, 2.3%) had induced labor. Conclusions: Congenital choledochal cysts of fetuses can be detected by prenatal ultrasonography and are curable. Patients having surgical treatment timely and early after birth will have a good prognosis. Delayed surgery can cause irreversible damage to the liver.
张普庆，吴青青，王 莉，梁 娜，韩吉晶，张铁娟，马玉庆，姚 苓，孙 娟. 胎儿先天性胆总管囊肿的产前超声诊断及预后评估[J]. 中国临床医学影像杂志, 2019, 30(1): 36-38.
ZHANG Pu-qing, WU Qing-qing, WANG Li, LIANG Na, HAN Ji-jing, ZHANG Tei-juan,. The prenatal ultrasound diagnosis and evaluation of the prognosis of fetal congenital choledochal cysts. JOURNAL OF CHINA MEDICAL IMAGING, 2019, 30(1): 36-38.
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